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法洛四联症包括哪四种
更新时间: 2020-09-27 00:00:00  

法洛四联症是一种常见的先天性心脏畸形,包括室间隔缺损、肺动脉狭窄、主动脉骑跨和右心室肥厚。法洛四联症在儿童发绀型心脏畸形中居首位。

法洛四联症患儿的预后主要取决定肺动脉狭窄程度及侧支循环情况,重症者有25%到35%在1岁内死亡,50%病人死于3岁内,70%到75%死于10岁内,90%病人会夭折。主要是由于慢性缺氧引起,红细胞增多症,导致继发性心肌肥大和心力衰竭而死亡。

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